Gene: EBF3
Alternate names for this Gene: COE3|EBF-3|HADDS|O/E-2|OE-2
Gene Summary: This gene encodes a member of the early B-cell factor (EBF) family of DNA binding transcription factors. EBF proteins are involved in B-cell differentiation, bone development and neurogenesis, and may also function as tumor suppressors. The encoded protein inhibits cell survival through the regulation of genes involved in cell cycle arrest and apoptosis, and aberrant methylation or deletion of this gene may play a role in multiple malignancies including glioblastoma multiforme and gastric carcinoma.
Gene is located in Chromosome: 10
Location in Chromosome : 10q26.3
Description of this Gene: EBF transcription factor 3
Type of Gene: protein-coding
rs1057519389 in
EBF3 gene and
Abnormal palmar creases
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Abnormality of facial musculature
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Aplasia/Hypoplasia of the cerebellar vermis
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Apraxias
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Ataxia
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Cerebellar Ataxia
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Clinodactyly of the 5th finger
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Deglutition Disorders
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Dysarthria
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1131692261 in
EBF3 gene and
Dysmorphic features
PMID 29162653 2017 De novo variants in EBF3 are associated with hypotonia, developmental delay, intellectual disability, and autism.
PMID 29062322 2017 Whole Gene Deletion of EBF3 Supporting Haploinsufficiency of This Gene as a Mechanism of Neurodevelopmental Disease.
PMID 20300201 2010 Mutations in ARX Result in Several Defects Involving GABAergic Neurons.
PMID 19627984 2009 Arx acts as a regional key selector gene in the ventral telencephalon mainly through its transcriptional repression activity.
PMID 28017370 2017 De Novo Mutations in EBF3 Cause a Neurodevelopmental Syndrome.
PMID 28017373 2017 Mutations in EBF3 Disturb Transcriptional Profiles and Cause Intellectual Disability, Ataxia, and Facial Dysmorphism.
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
PMID 28487885 2017 Novel de novo variant in EBF3 is likely to impact DNA binding in a patient with a neurodevelopmental disorder and expanded phenotypes: patient report, in silico functional assessment, and review of published cases.
rs1057519389 in
EBF3 gene and
Expressive language delay
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Generalized hypotonia
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Global developmental delay
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs779003155 in
EBF3 gene and
HYPOTONIA, ATAXIA, AND DELAYED DEVELOPMENT SYNDROME
PMID 28017370 2017 De Novo Mutations in EBF3 Cause a Neurodevelopmental Syndrome.
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
PMID 28017373 2017 Mutations in EBF3 Disturb Transcriptional Profiles and Cause Intellectual Disability, Ataxia, and Facial Dysmorphism.
rs1057519389 in
EBF3 gene and
Hypoplastic feet
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Impaired pain sensation
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Movement Disorders
PMID 28487885 2017 Novel de novo variant in EBF3 is likely to impact DNA binding in a patient with a neurodevelopmental disorder and expanded phenotypes: patient report, in silico functional assessment, and review of published cases.
PMID 19627984 2009 Arx acts as a regional key selector gene in the ventral telencephalon mainly through its transcriptional repression activity.
PMID 28017373 2017 Mutations in EBF3 Disturb Transcriptional Profiles and Cause Intellectual Disability, Ataxia, and Facial Dysmorphism.
PMID 28017370 2017 De Novo Mutations in EBF3 Cause a Neurodevelopmental Syndrome.
PMID 20300201 2010 Mutations in ARX Result in Several Defects Involving GABAergic Neurons.
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
PMID 29162653 2017 De novo variants in EBF3 are associated with hypotonia, developmental delay, intellectual disability, and autism.
PMID 29062322 2017 Whole Gene Deletion of EBF3 Supporting Haploinsufficiency of This Gene as a Mechanism of Neurodevelopmental Disease.
rs1057519389 in
EBF3 gene and
Muscle hypotonia
PMID 20300201 2010 Mutations in ARX Result in Several Defects Involving GABAergic Neurons.
PMID 19627984 2009 Arx acts as a regional key selector gene in the ventral telencephalon mainly through its transcriptional repression activity.
PMID 29062322 2017 Whole Gene Deletion of EBF3 Supporting Haploinsufficiency of This Gene as a Mechanism of Neurodevelopmental Disease.
PMID 28487885 2017 Novel de novo variant in EBF3 is likely to impact DNA binding in a patient with a neurodevelopmental disorder and expanded phenotypes: patient report, in silico functional assessment, and review of published cases.
PMID 29162653 2017 De novo variants in EBF3 are associated with hypotonia, developmental delay, intellectual disability, and autism.
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
PMID 28017370 2017 De Novo Mutations in EBF3 Cause a Neurodevelopmental Syndrome.
PMID 28017373 2017 Mutations in EBF3 Disturb Transcriptional Profiles and Cause Intellectual Disability, Ataxia, and Facial Dysmorphism.
rs1057519389 in
EBF3 gene and
Oligohydramnios
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Overfolding of the superior helices
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Pierre Robin Syndrome
PMID 28017370 2017 De Novo Mutations in EBF3 Cause a Neurodevelopmental Syndrome.
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Poor school performance
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Small labia majora
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Stereotypic Movement Disorder
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Strabismus
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Torticollis
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.
rs1057519389 in
EBF3 gene and
Triangular face
PMID 28017372 2017 A Syndromic Neurodevelopmental Disorder Caused by De Novo Variants in EBF3.