Gene: HIBADH
Alternate names for this Gene: NS5ATP1
Gene Summary: This gene encodes a mitochondrial 3-hydroxyisobutyrate dehydrogenase enzyme. The encoded protein plays a critical role in the catabolism of L-valine by catalyzing the oxidation of 3-hydroxyisobutyrate to methylmalonate semialdehyde.
Gene is located in Chromosome: 7
Location in Chromosome : 7p15.2
Description of this Gene: 3-hydroxyisobutyrate dehydrogenase
Type of Gene: protein-coding