Gene: HPS4
Alternate names for this Gene: BLOC3S2|LE
Gene Summary: This gene encodes a protein component of biogenesis of lysosome-related organelles complexes (BLOC). BLOC complexes are important for the formation of endosomal-lysosomal organelles such as melanosomes and platelet dense granules. Mutations in this gene result in subtype 4 of Hermansky-Pudlak syndrome, a form of albinism. Alternative splicing results in multiple transcript variants.
Gene is located in Chromosome: 22
Location in Chromosome : 22q12.1
Description of this Gene: HPS4 biogenesis of lysosomal organelles complex 3 subunit 2
Type of Gene: protein-coding