Gene: UTP4
Alternate names for this Gene: CIRH1A|CIRHIN|NAIC|TEX292
Gene Summary: This gene encodes a WD40-repeat-containing protein that is localized to the nucleolus. Mutation of this gene causes North American Indian childhood cirrhosis, a severe intrahepatic cholestasis that results in transient neonatal jaundice, and progresses to periportal fibrosis and cirrhosis in childhood and adolescence. Alternative splicing results in multiple transcript variants.
Gene is located in Chromosome: 16
Location in Chromosome : 16q22.1
Description of this Gene: UTP4 small subunit processome component
Type of Gene: protein-coding