Condition: Bile acid synthesis defect, congenital, 1


rs104894518 in HSD3B7 gene and Bile acid synthesis defect, congenital, 1 PMID 11067870 2000 The bile acid synthetic gene 3beta-hydroxy-Delta(5)-C(27)-steroid oxidoreductase is mutated in progressive intrahepatic cholestasis.

PMID 12679481 2003 Molecular genetics of 3beta-hydroxy-Delta5-C27-steroid oxidoreductase deficiency in 16 patients with loss of bile acid synthesis and liver disease.