PMID 24535794 2014 C to T transition at position 1108 (c.1108 C > T) in exon 6, causing stop codon formation (R370X) was seen in the HTRA1 gene in a homozygous state in the CARASIL patient whereas it was heterozygous in other healthy family members.
PMID 21482952 2011 A novel mutation in the HTRA1 gene causes CARASIL without alopecia.
PMID 22900900 2012 A novel mutation in the HTRA1 gene identified in Chinese CARASIL pedigree.