Condition: Leigh syndrome , French Canadian type


rs119466000 in LRPPRC gene and Leigh syndrome , French Canadian type PMID 12529507 2003 Identification of a gene causing human cytochrome c oxidase deficiency by integrative genomics.

PMID 21266382 2011 LRPPRC mutations cause a phenotypically distinct form of Leigh syndrome with cytochrome c oxidase deficiency.

PMID 17050673 2006 Defects in energy homeostasis in Leigh syndrome French Canadian variant through PGC-1alpha/LRP130 complex.

PMID 29152527 2019 Novel LRPPRC Mutation in a Boy With Mild Leigh Syndrome, French-Canadian Type Outside of Québec.