Condition: MITOCHONDRIAL DNA DEPLETION SYNDROME 8A (ENCEPHALOMYOPATHIC TYPE WITH RENAL TUBULOPATHY)


rs121918308 in RRM2B gene and MITOCHONDRIAL DNA DEPLETION SYNDROME 8A (ENCEPHALOMYOPATHIC TYPE WITH RENAL TUBULOPATHY) PMID 17486094 2007 Mutation of RRM2B, encoding p53-controlled ribonucleotide reductase (p53R2), causes severe mitochondrial DNA depletion.

PMID 18504129 2008 Mitochondrial DNA depletion syndrome due to mutations in the RRM2B gene.

PMID 19667227 2009 Mitochondrial neurogastrointestinal encephalopathy due to mutations in RRM2B.