Condition: SHORT STATURE, OPTIC NERVE ATROPHY, AND PELGER-HUET ANOMALY
rs369698072
in
NBAS
gene and
SHORT STATURE, OPTIC NERVE ATROPHY, AND PELGER-HUET ANOMALY
PMID 20577004
2010 Subsequently, 33 of 34 patients were identified with
SOPH syndrome
and had a
5741G/A
nucleotide substitution (resulting in the amino acid substitution
R1914H
) in the NBAS gene in the homozygous state.
PMID 26073778
2015 Biallelic Mutations in NBAS Cause Recurrent Acute Liver Failure with Onset in Infancy.